Pesquisa sobre: PHOSPHOFRUCTOKINASE-1, MUSCLE TYPE 
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Descritor Inglês:   Phosphofructokinase-1, Muscle Type 
Descritor Espanhol:   fosfofructocinasa-1 tipo muscular 
Descritor Português:   Fosfofrutoquinase-1 Muscular 
Sinônimos Inglês:   6-Phosphofructokinase, Muscle Type
Phosphofructo-1-kinase Isozyme A
Phosphofructokinase 1, Muscle Type  
Categoria:   D08.811.913.696.620.225.850.500.500
Definição Inglês:   An allosteric enzyme that regulates glycolysis by catalyzing the transfer of a phosphate group from ATP to fructose-6-phosphate to yield fructose-1,6-bisphosphate. In humans, PHOSPHOFRUCTOKINASE-1 in muscle exists as the homotetramer of M subunits. Defects in this muscle enzyme cause GLYCOGEN STORAGE DISEASE TYPE VII, also known as Tarui's disease. 
Combinados Inglês:   Phosphofructokinase-1, Muscle Type/deficiency use Glycogen Storage Disease Type VII
 
Nota Histórica Inglês:   2002 
Qualificadores Permitidos Inglês:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Número do Registro:   36114 
Identificador Único:   D025203 

Ocorrência na BVS:
 

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